Race
United States statistics
Age
Sex
International statistics
Hirschsprung disease is uncommon in premature infants. However, the age at which Hirschsprung disease is diagnosed has progressively decreased over the past century. In the early 1900s, the median age at diagnosis was 2-3 years; from the 1950s to 1970s, the median age was 2-6 months.
Although the exact worldwide incidence is unknown, international studies have reported rates ranging from approximately 1 case per 1500-7000 newborns.
Hirschsprung disease affects all races; however, it is roughly 3 times more common among Asian- Americans.
Hirschsprung disease affects approximately 1 case per 5400-7200 newborns annually.
This disease occurs more often in males than in females, with a male-to-female ratio of approximately 4:1; however, the ratio in long-segment disease decreases to 2:1.
