Encourage tobacco users to quit and offer pharmacotherapy as needed.
Immunosuppressant agents (eg, azathioprine, cyclophosphamide)
Tyrosine kinase inhibitors (eg, nintedanib)
Prescribe oxygen therapy in patients with hypoxemia at rest or with exercise (partial pressure of oxygen [PaO2] < 55 mmHg or an oxygen saturation by pulse oximetry [SpO2] < 88%). The goal is to maintain an oxygen saturation of at least 90% at rest, with sleep, and with exertion.
Systemic corticosteroids (eg, prednisone)
Vaccinate patients against influenza and pneumococcal infection.
Antifibrotic agents (eg, pirfenidone)
